Ectopia cordis

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Figer-1

📄 Report Sample Line- Ectopia cordis (During First Trimester / NT Screening)
The fetal heart is visualized partially/completely outside the thoracic cavity on anterior chest wall, consistent with ectopia cordis. There is a midline thoracic wall defect with abnormal cardiac position and motion outside the thorax.


Conclussion: 📋 Sonographic findings are diagnostic of ectopia cordis.
Recommendation: Follow-up MRI

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Note: Select English to answer in English, या हिंदी चुनें तो प्रश्नों के उत्तर हिंदी में दीजिए।

1. What is ectopia cordis? 1. एक्टोपिया कॉर्डिस क्या है?
A. Congenital malposition of the heart partially or completely outside the thoracic cavity n
B. Normal fetal heart position
C. Herniation of abdominal contents only
D. Isolated pericardial effusion

2. Ectopia cordis is most commonly associated with which other defect? 2. एक्टोपिया कॉर्डिस सबसे सामान्यतः किस अन्य दोष के साथ जुड़ा होता है?
A. Ventral wall defects (eg omphalocele), as part of pentalogy of Cantrell spectrum
B. Isolated limb lengthening
C. Maternal placental abruption
D. Only neural tube defects

3. Prenatal ultrasound appearance of ectopia cordis often shows: 3. गर्भकालीन अल्ट्रासाउंड पर एक्टोपिया कॉर्डिस का रूप कैसा दिखता है?
A. Heart located anterior to the chest wall or entirely outside the thorax with abnormal thoracic contour
B. Normal cardiac position with small ventricles
C. Only abdominal free fluid
D. Enlarged fetal kidneys only

4. Ectopia cordis prognosis depends mainly on: 4. एक्टोपिया कॉर्डिस का पूर्वानुमान मुख्यतः किन बातों पर निर्भर करता है?
A. Degree of thoracic involvement, intracardiac defects, and associated anomalies
B. Maternal blood pressure only
C. Fetal gender only
D. Placental weight only

5. Which type of ectopia cordis carries the worst prognosis? 5. किस प्रकार का एक्टोपिया कॉर्डिस सबसे खराब पूर्वानुमान रखता है?
A. Thoracoabdominal or extensive defects with major intracardiac anomalies
B. Small isolated pericardial ectopia with normal heart
C. Ectopia of limbs
D. Only skin discoloration

6. Best prenatal evaluation when ectopia cordis is suspected includes: 6. जब एक्टोपिया कॉर्डिस का संदेह हो तो सर्वोत्तम गर्भकालीन मूल्यांकन में क्या शामिल होना चाहिए?
A. Detailed fetal echocardiography, targeted anatomic survey for midline and thoracoabdominal defects, and genetic counseling/testing
B. Only maternal ECG
C. No further tests
D. Immediate induction without evaluation

7. Which associated syndrome includes ectopia cordis as a feature? 7. किस संबंधित सिंड्रोम में एक्टोपिया कॉर्डिस एक लक्षण के रूप में शामिल है?
A. Pentalogy of Cantrell (involves lower sternum defect, diaphragmatic defect, pericardial defect, intracardiac anomalies, and abdominal wall defect)
B. Down syndrome only
C. Maternal gestational diabetes
D. Isolated clubfoot

8. Delivery planning for a fetus with ectopia cordis should include: 8. एक्टोपिया कॉर्डिस वाले भ्रूण के लिए डिलीवरी योजना में क्या शामिल होना चाहिए?
A. Delivery at tertiary center with neonatal surgical and cardiothoracic support and multidisciplinary team
B. Home birth always
C. No special planning
D. Immediate termination without counseling

9. Postnatal management may require which of the following? 9. प्रसवोपरांत प्रबंधन में निम्नलिखित में से कौन-सी चीज़ों की आवश्यकता हो सकती है?
A. Immediate airway and cardiac stabilization, protective coverage of the heart, and staged surgical repair if feasible
B. No interventions ever
C. Routine vaccination only
D. Maternal antibiotics only

10. Prenatal detection of ectopia cordis allows which benefit? 10. एक्टोपिया कॉर्डिस का गर्भकालीन पता लगाने से कौन सा लाभ होता है?
A. Enables multidisciplinary counseling, delivery planning at an appropriate center, and parental decision-making
B. Guarantees fetal cure in utero
C. No impact on care
D. Always maternal surgery